Gigantic vascular anomaly in a PHACE syndrome patient managed with photodynamic therapy.

Vascular anomalies are congenital vascular tissue aberrations, hich are commonly identified in the head and neck and known to ffect approximately 1 in 22 children. The most recent classificaion of vascular anomalies includes two main categories: vascular umours (haemangiomas) and vascular malformations [1]. Several problems can arise from vascular tumours, including unctional (through mass effect), aesthetic impairment, pain, bleedng (platelet sequestration) and disability [2]. They are known to e associated with a number of syndromes involving the head and eck, including PHACE (posterior fossa malformations – haemaniomas – arterial anomalies – cardiac defects – eye abnormalities) 3]. PHACE syndrome is a rare association between cervicofacial aemangiomas, structural brain abnormalities (mainly of the poserior fossa), arterial and cerebrovascular anomalies, aortic and ardiac abnormalities as well as eye defects. It represents a fairly ommon syndrome, identified in 1996 and more common in emales. The haemangioma component in PHACE is very small or